Q23.4 Hypoplastic left heart syndrome

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for Hypoplastic left heart syndrome is Q23.4 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
Q20-Q28: Congenital malformations of the circulatory system (Q20-Q28)
Category Q23
11 codes (9 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q23.4:

  • Syndrome › hypoplastic left-heart
  • Hypoplasia, hypoplastic › left heart syndrome
  • Hypoplasia, hypoplastic › aorta, aortic › ascending, in hypoplastic left heart syndrome
  • Atresia, atretic › mitral valve › in hypoplastic left heart syndrome
  • Atresia, atretic › aortic (orifice) (valve) › congenital with hypoplasia of ascending aorta and defective development of left ventricle (with mitral stenosis)
  • Atresia, atretic › aortic (orifice) (valve) › in hypoplastic left heart syndrome
  • Development › defective, congenital › left ventricle › in hypoplastic left heart syndrome
  • Hypoplasia, hypoplastic › aorta, aortic › valve › in hypoplastic left heart syndrome

U.S. Hospital Utilization

  • An estimated 6,040 U.S. inpatient stays in 2023 included Q23.4 among the documented diagnoses.
  • 1,725 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section III

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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