Q21.22 Transitional atrioventricular septal defect

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for Transitional atrioventricular septal defect is Q21.22 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
Q20-Q28: Congenital malformations of the circulatory system (Q20-Q28)
Category Q21
20 codes (17 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q21.22:

  • Defect, defective › cushion, endocardial › intermediate
  • Canal › atrioventricular › intermediate
  • Canal › atrioventricular › transitional
  • Defect, defective › cushion, endocardial › transitional
  • Defect, defective › atrioventricular › septal › transitional
  • Defect, defective › atrioventricular › septal › intermediate
  • Defect, defective › atrial septal › ostium primum type (type I) › with › separate atrioventricular valves › and small or restrictive inlet VSD

Inclusion Terms

  • Intermediate atrioventricular canal
  • Intermediate atrioventricular septal defect
  • Intermediate endocardial cushion defect
  • Ostium primum atrial septal defect (type I) with separate atrioventricular valves and a small or restrictive inlet VSD
  • Transitional atrioventricular canal
  • Transitional endocardial cushion defect

U.S. Hospital Utilization

  • An estimated 600 U.S. inpatient stays in 2023 included Q21.22 among the documented diagnoses.
  • 220 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section III

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Search all 70,000+ ICD-10-CM codes →
Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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