Q07.03 Arnold-Chiari syndrome with spina bifida and hydrocephalus

The ICD-10-CM code for Arnold-Chiari syndrome with spina bifida and hydrocephalus is Q07.03 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

17: Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

Section

Q00-Q07: Congenital malformations of the nervous system (Q00-Q07)

Category Q07

8 codes (6 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q07.03:

• Arnold-Chiari disease, obstruction or syndrome (type II) › with › hydrocephalus › with spina bifida
• Arnold-Chiari disease, obstruction or syndrome (type II) › with › spina bifida › with hydrocephalus

U.S. Hospital Utilization

• An estimated 3,820 U.S. inpatient stays in 2023 included Q07.03 among the documented diagnoses.
• 330 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)