N07.B Hereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD]

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for Hereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD] is N07.B (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
N00-N08: Glomerular diseases (N00-N08)
Category N07
13 codes (12 billable)
FY2026 Status
New code in FY2026

Also Known As

ICD-10-CM Alphabetic Index entries that lead to N07.B:

  • AMKD (APOL1-mediated kidney disease) (with glomerulonephritis) (with glomerulosclerosis)
  • Nephropathy › hereditary NEC › with › APOL1-mediated kidney disease (AMKD)

Inclusion Terms

  • AMKD (with glomerulonephritis)
  • AMKD (with glomerulosclerosis)

Official Coding Guidelines

CKD staging and code assignment (N18.-)

The ICD-10-CM classifies CKD based on severity. The severity of CKD is designated by stages 1-5. Stage 2, code N18.2, equates to mild CKD; stage 3, codes N18.30-N18.32, equate to moderate CKD; and stage 4, code N18.4, equates to severe CKD. Code N18.6, End stage renal disease (ESRD), is assigned when the provider has documented end- stage renal disease (ESRD).

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.14.a.1
CKD stage plus ESRD: assign N18.6 only

If both a stage of CKD and ESRD are documented, assign code N18.6 only.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.14.a.1

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Parent Code

N07 Hereditary nephropathy, not elsewhere classified

Related Codes in N07

N07 Hereditary nephropathy, not elsewhere classified N07.0 Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality N07.1 Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions N07.2 Hereditary nephropathy, not elsewhere classified with diffuse membranous glomerulonephritis N07.3 Hereditary nephropathy, not elsewhere classified with diffuse mesangial proliferative glomerulonephritis N07.4 Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis N07.5 Hereditary nephropathy, not elsewhere classified with diffuse mesangiocapillary glomerulonephritis N07.6 Hereditary nephropathy, not elsewhere classified with dense deposit disease N07.7 Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis N07.8 Hereditary nephropathy, not elsewhere classified with other morphologic lesions N07.9 Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions N07.A Hereditary nephropathy, not elsewhere classified with C3 glomerulonephritis
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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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