N04.6 Nephrotic syndrome with dense deposit disease

The ICD-10-CM code for Nephrotic syndrome with dense deposit disease is N04.6 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

14: Diseases of the genitourinary system (N00-N99)

Section

N00-N08: Glomerular diseases (N00-N08)

Category N04

19 codes (16 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to N04.6:

• Syndrome › nephrotic (congenital) › with › dense deposit disease
• Syndrome › nephrotic (congenital) › with › C3 › glomerulopathy › with dense deposit disease

Inclusion Terms

• Nephrotic syndrome with C3 glomerulopathy with dense deposit disease
• Nephrotic syndrome with membranoproliferative glomerulonephritis, type 2

U.S. Hospital Utilization

N04.6 appeared in too few sampled U.S. inpatient stays in 2023 to report a national estimate (AHRQ suppresses counts of 10 or fewer) — a rare inpatient diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

CKD staging and code assignment (N18.-)

The ICD-10-CM classifies CKD based on severity. The severity of CKD is designated by stages 1-5. Stage 2, code N18.2, equates to mild CKD; stage 3, codes N18.30-N18.32, equate to moderate CKD; and stage 4, code N18.4, equates to severe CKD. Code N18.6, End stage renal disease (ESRD), is assigned when the provider has documented end- stage renal disease (ESRD).

CKD stage plus ESRD: assign N18.6 only

If both a stage of CKD and ESRD are documented, assign code N18.6 only.

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)