N01.9 Rapidly progressive nephritic syndrome with unspecified morphologic changes

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for Rapidly progressive nephritic syndrome with unspecified morphologic changes is N01.9 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
N00-N08: Glomerular diseases (N00-N08)
Category N01
12 codes (11 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to N01.9:

  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › rapidly progressive
  • Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › subacute
  • Glomerulonephritis › rapidly progressive
  • Glomerulonephritis › subacute
  • Disease, diseased › glomerular › rapidly progressive
  • Disease, diseased › renal (functional) (pelvis) › subacute
  • Disease, diseased › renal (functional) (pelvis) › rapidly progressive
  • Glomerulonephritis › poststreptococcal NEC › rapidly progressive

U.S. Hospital Utilization

  • An estimated 880 U.S. inpatient stays in 2023 included N01.9 among the documented diagnoses.
  • 180 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

CKD staging and code assignment (N18.-)

The ICD-10-CM classifies CKD based on severity. The severity of CKD is designated by stages 1-5. Stage 2, code N18.2, equates to mild CKD; stage 3, codes N18.30-N18.32, equate to moderate CKD; and stage 4, code N18.4, equates to severe CKD. Code N18.6, End stage renal disease (ESRD), is assigned when the provider has documented end- stage renal disease (ESRD).

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.14.a.1
CKD stage plus ESRD: assign N18.6 only

If both a stage of CKD and ESRD are documented, assign code N18.6 only.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.14.a.1

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Parent Code

N01 Rapidly progressive nephritic syndrome

Related Codes in N01

N01 Rapidly progressive nephritic syndrome N01.0 Rapidly progressive nephritic syndrome with minor glomerular abnormality N01.1 Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions N01.2 Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis N01.3 Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis N01.4 Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis N01.5 Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis N01.6 Rapidly progressive nephritic syndrome with dense deposit disease N01.7 Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis N01.8 Rapidly progressive nephritic syndrome with other morphologic changes N01.A Rapidly progressive nephritic syndrome with C3 glomerulonephritis
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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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