M35.81 Multisystem inflammatory syndrome

✓ Billable ICD-10-CM 2026
Open M35.81 in Web App →

The ICD-10-CM code for Multisystem inflammatory syndrome is M35.81 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
M30-M36: Systemic connective tissue disorders (M30-M36)
Category M35
26 codes (23 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to M35.81:

  • MIS-C
  • Multisystem inflammatory syndrome (in adult) (in children)
  • PIMS
  • Pediatric inflammatory multisystem syndrome
  • MIS-A
  • Syndrome › pediatric inflammatory multisystem
  • Syndrome › multisystem inflammatory (in adults) (in children)
Code First
  • , if applicable, COVID-19 (U07.1)
Code Also
  • any associated complications such as:
  • acute hepatic failure (K72.0-)
  • acute kidney failure (N17.-)
  • acute myocarditis (I40.-)
  • acute respiratory distress syndrome (J80)
  • cardiac arrhythmia (I47-I49.-)
  • pneumonia due to COVID-19 (J12.82)
  • severe sepsis (R65.2-)
  • viral cardiomyopathy (B33.24)
  • viral pericarditis (B33.23)
Use Additional Code
  • code, if applicable, for:
  • exposure to COVID-19 or SARS-CoV-2 infection (Z20.822)
  • personal history of COVID-19 (Z86.16)
  • post COVID-19 condition (U09.9)

Inclusion Terms

  • MIS-A
  • MIS-C
  • Multisystem inflammatory syndrome in adults
  • Multisystem inflammatory syndrome in children
  • Pediatric inflammatory multisystem syndrome
  • PIMS

U.S. Hospital Utilization

  • An estimated 1,445 U.S. inpatient stays in 2023 included M35.81 among the documented diagnoses.
  • 430 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

MIS with COVID-19: U07.1 principal/first-listed + M35.81 addl

(l) Multisystem Inflammatory Syndrome For individuals with multisystem inflammatory syndrome (MIS) and COVID-19, assign code U07.1, COVID-19, as the principal/first-listed diagnosis and assign code M35.81, Multisystem inflammatory syndrome, as an additional diagnosis.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.1.g.1.l
History of COVID-19 develops MIS: assign M35.81 and U09.9

If an individual with a history of COVID-19 develops MIS, assign codes M35.81, Multisystem inflammatory syndrome, and U09.9, Post COVID-19 condition, unspecified.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.1.g.1.l

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Search all 70,000+ ICD-10-CM codes →
Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

Get HCC Mappings, Clinical Summaries, and More

Access premium features including HCC risk adjustment, FDA drug indications, AI coding assistant, and comprehensive clinical context.

Start Free Trial