I27.1 Kyphoscoliotic heart disease
The ICD-10-CM code for Kyphoscoliotic heart disease is I27.1 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- I26-I28: Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)
- Category I27
- 21 codes (17 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to I27.1:
- Kyphoscoliosis, kyphoscoliotic (acquired) › heart (disease)
- Disease, diseased › heart (organic) › kyphoscoliotic
- Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) › pulmonary › due to › kyphoscoliotic heart disease
U.S. Hospital Utilization
I27.1 appeared in too few sampled U.S. inpatient stays in 2023 to report a national estimate (AHRQ suppresses counts of 10 or fewer) — a rare inpatient diagnosis.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Pulmonary Hypertension11) Pulmonary Hypertension Pulmonary hypertension is classified to category I27, Other pulmonary heart diseases. For secondary pulmonary hypertension (I27.1, I27.2-), code also any associated conditions or adverse effects of drugs or toxins. The sequencing is based on the reason for the encounter, except for adverse effects of drugs (See Section I.C.19.e.).
Presumed relationship due to Index term “with”The classification presumes a causal relationship between hypertension and heart involvement and between hypertension and kidney involvement, as the two conditions are linked by the term “with” in the Alphabetic Index. These conditions should be coded as related even in the absence of provider documentation explicitly linking them, unless the documentation clearly states the conditions are unrelated.
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026