H57.01 Argyll Robertson pupil, atypical

The ICD-10-CM code for Argyll Robertson pupil, atypical is H57.01 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

7: Diseases of the eye and adnexa (H00-H59)

Section

H55-H57: Other disorders of eye and adnexa (H55-H57)

Category H57

31 codes (24 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to H57.01:

• Anomaly, anomalous (congenital) (unspecified type) › pupil › function › Argyll Robertson pupil

U.S. Hospital Utilization

H57.01 appeared in too few sampled U.S. inpatient stays in 2023 to report a national estimate (AHRQ suppresses counts of 10 or fewer) — a rare inpatient diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Glaucoma (TOC entry)

a. Glaucoma .............................................................................................................................. 48

Assigning glaucoma codes (use as many H40 codes as needed)

Assign as many codes from category H40, Glaucoma, as needed to identify the type of glaucoma, the affected eye, and the glaucoma stage.

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)