G90.3 Multi-system degeneration of the autonomic nervous system

The ICD-10-CM code for Multi-system degeneration of the autonomic nervous system is G90.3 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

6: Diseases of the nervous system (G00-G99)

Section

G89-G99: Other disorders of the nervous system (G89-G99)

Category G90

27 codes (21 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to G90.3:

• Shy-Drager syndrome
• Degeneration, degenerative › multi-system
• Hypotension (arterial) (constitutional) › neurogenic, orthostatic
• Parkinsonism (idiopathic) (primary) › with neurogenic orthostatic hypotension (symptomatic)
• Hypotension (arterial) (constitutional) › orthostatic (chronic) › neurogenic

Inclusion Terms

• Neurogenic orthostatic hypotension [Shy-Drager]

U.S. Hospital Utilization

• An estimated 7,445 U.S. inpatient stays in 2023 included G90.3 among the documented diagnoses.
• 2,235 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Dominant/nondominant side (TOC entry)

a. Dominant/nondominant side ................................................................................................. 45

Pain - Category G89 (TOC entry)

b. Pain - Category G89.............................................................................................................. 45

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)