G23.3 Hypomyelination with atrophy of the basal ganglia and cerebellum

The ICD-10-CM code for Hypomyelination with atrophy of the basal ganglia and cerebellum is G23.3 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

6: Diseases of the nervous system (G00-G99)

Section

G20-G26: Extrapyramidal and movement disorders (G20-G26)

Category G23

7 codes (6 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to G23.3:

• Hypomyelination with atrophy of the basal ganglia and cerebellum (H-ABC)
• H-ABC (hypomyelination with atrophy of the basal ganglia and cerebellum)
• Disorder (of) › neurological NEC › TUBB4A-related

Inclusion Terms

• H-ABC
• TUBB4A-related neurologic disorders

U.S. Hospital Utilization

G23.3 appeared in too few sampled U.S. inpatient stays in 2023 to report a national estimate (AHRQ suppresses counts of 10 or fewer) — a rare inpatient diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Dominant/nondominant side (TOC entry)

a. Dominant/nondominant side ................................................................................................. 45

Pain - Category G89 (TOC entry)

b. Pain - Category G89.............................................................................................................. 45

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)