G11.19 Other early-onset cerebellar ataxia

The ICD-10-CM code for Other early-onset cerebellar ataxia is G11.19 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

6: Diseases of the nervous system (G00-G99)

Section

G10-G14: Systemic atrophies primarily affecting the central nervous system (G10-G14)

Category G11

13 codes (11 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to G11.19:

• Ataxia, ataxy, ataxic › spinocerebellar, X-linked recessive
• Ramsay-Hunt disease or syndrome › meaning dyssynergia cerebellaris myoclonica
• Ataxia, ataxy, ataxic › Hunt's
• Dyssynergia › cerebellaris myoclonica (Hunt's ataxia)
• Syndrome › Hunt's (herpetic geniculate ganglionitis) (neuralgia) › dyssynergia cerebellaris myoclonica
• Disease, diseased › Hunt's (herpetic geniculate ganglionitis) (neuralgia) › dyssynergia cerebellaris myoclonica
• Hunt's › disease or syndrome (herpetic geniculate ganglionitis) › dyssynergia cerebellaris myoclonica
• Ataxia, ataxy, ataxic › cerebellar (hereditary) › with › essential tremor

Inclusion Terms

• Early-onset cerebellar ataxia with essential tremor
• Early-onset cerebellar ataxia with myoclonus [Hunt's ataxia]
• Early-onset cerebellar ataxia with retained tendon reflexes
• X-linked recessive spinocerebellar ataxia

U.S. Hospital Utilization

• An estimated 695 U.S. inpatient stays in 2023 included G11.19 among the documented diagnoses.
• 115 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Dominant/nondominant side (TOC entry)

a. Dominant/nondominant side ................................................................................................. 45

Pain - Category G89 (TOC entry)

b. Pain - Category G89.............................................................................................................. 45

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)