E03.0 Congenital hypothyroidism with diffuse goiter

The ICD-10-CM code for Congenital hypothyroidism with diffuse goiter is E03.0 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

4: Endocrine, nutritional and metabolic diseases (E00-E89)

Section

E00-E07: Disorders of thyroid gland (E00-E07)

Category E03

9 codes (8 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to E03.0:

• Goiter (plunging) (substernal) › congenital (nontoxic)
• Goiter (plunging) (substernal) › congenital (nontoxic) › diffuse
• Hypothyroidism (acquired) › congenital (without goiter) › with goiter (diffuse)
• Goiter (plunging) (substernal) › congenital (nontoxic) › parenchymatous

Inclusion Terms

• Congenital parenchymatous goiter (nontoxic)
• Congenital goiter (nontoxic) NOS

U.S. Hospital Utilization

• An estimated 165 U.S. inpatient stays in 2023 included E03.0 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Diabetes mellitus (TOC entry)

a. Diabetes mellitus ................................................................................................................... 39

Obesity (TOC entry)

b. Obesity .................................................................................................................................. 42

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)