D82.0 Wiskott-Aldrich syndrome

The ICD-10-CM code for Wiskott-Aldrich syndrome is D82.0 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

Section

D80-D89: Certain disorders involving the immune mechanism (D80-D89)

Category D82

8 codes (7 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to D82.0:

• Aldrich (-Wiskott) syndrome (eczema-thrombocytopenia)
• Wiskott-Aldrich syndrome
• Syndrome › familial eczema-thrombocytopenia (Wiskott-Aldrich)
• Syndrome › eczema-thrombocytopenia
• Syndrome › Wiskott-Aldrich
• Syndrome › Aldrich (-Wiskott)
• Immunodeficiency › with › thrombocytopenia and eczema
• Deficiency, deficient › immunity › cell-mediated › with thrombocytopenia and eczema

Inclusion Terms

• Immunodeficiency with thrombocytopenia and eczema

U.S. Hospital Utilization

• An estimated 235 U.S. inpatient stays in 2023 included D82.0 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Chapter 3 TOC entry

3. Chapter 3: Disease of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) ............................................................................................. 39

Reserved for future guideline expansion

Reserved for future guideline expansion ...................................................................................... 39

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)