D61.01 Constitutional (pure) red blood cell aplasia
The ICD-10-CM code for Constitutional (pure) red blood cell aplasia is D61.01 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- D60-D64: Aplastic and other anemias and other bone marrow failure syndromes (D60-D64)
- Category D61
- 17 codes (13 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to D61.01:
- Kaznelson's syndrome (congenital hypoplastic anemia)
- Joseph-Diamond-Blackfan anemia (congenital hypoplastic)
- Blackfan-Diamond anemia or syndrome (congenital hypoplastic anemia)
- Diamond-Blackfan anemia (congenital hypoplastic)
- Aplasia › congenital pure red cell
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › Joseph-Diamond-Blackfan (congenital hypoplastic)
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › Diamond-Blackfan (congenital hypoplastic)
- Aplasia › erythrocyte congenital
Inclusion Terms
- Blackfan-Diamond syndrome
- Congenital (pure) red cell aplasia
- Familial hypoplastic anemia
- Primary (pure) red cell aplasia
- Red cell (pure) aplasia of infants
U.S. Hospital Utilization
- An estimated 1,095 U.S. inpatient stays in 2023 included D61.01 among the documented diagnoses.
- 165 stays listed it as the principal diagnosis.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Chapter 3 TOC entry3. Chapter 3: Disease of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) ............................................................................................. 39
Reserved for future guideline expansionReserved for future guideline expansion ...................................................................................... 39
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026